1.Gouty Synovitis of the Knee with Partial Hypoxanthine-guanine Phosphoribosyl Transferase Deficiency (Kelley-Seegmiller Syndrome): A Case Report
Tsuyoshi Ohishi ; Tetsuya Ichikawa ; Michihito Miyagi ; Hiroshi Irisawa ; Akira Nagano
Journal of Rural Medicine 2008;4(2):80-83
We present here a case of gouty synovitis of the knee in a patient with partial hypoxanthine-guanine phosphoribosyl transferase deficiency (Kelley-Seegmiller syndrome), which is an inherited purine metabolic disorder. Magnetic resonance images and computed tomography showed a diffuse mass with stippled calcification around the posterior cruciate ligament (PCL) in the posterior intercondylar notch. Arthroscopic examination revealed that the articular surfaces and menisci in the affected knee were almost completely covered with white chalky monosodium urate (MSU) crystals. The diffuse mass around the PCL was composed of proliferative synovial villi covered with MSU crystals that looked like "snow covered trees". Arthroscopic total synovectomy was performed. The posterior trans-septal portal was especially useful for removal of the proliferative villi around the PCL. To our knowledge, this is the first report of arthroscopic examination in a patient with Kelley-Seegmiller syndrome.
Knee
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Posters [Publication Type]
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Transferases
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Synovitis
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Syndrome
2.Post viral acute multifocal posterior placoid pigment epithiopathy in a teenage child.
Angeline D C Nga ; N Ramli ; Z Mimiwati
The Medical journal of Malaysia 2009;64(2):176-8
We report a rare case of a young boy presenting with bilateral blurring of vision following a viral like illness. Fundus examination revealed multiple pale cream-coloured lesions scattered across the posterior pole of both eyes. Fundus fluorescein angiography showed characteristic features of early hypofluorescence and late hyperfluorescence, further confirming the diagnosis of acute posterior placoid pigment epitheliopathy (AMPPPE). He was treated with topical steroids for the accompanying mild anterior uveitis. He had a prompt visual recovery with no adverse sequelae.
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Viral
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Acute
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Pigments
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After values
3.An unusual radiographic presentation of posterior cruciate ligament avulsion fracture.
M N Mohd Nizlan ; A Suhail ; O C Samsudin ; O Masbah
The Medical journal of Malaysia 2004;59 Suppl F():65-8
A case of traumatic posterior cruciate ligament (PCL) avulsion fracture presenting with unusual radiographic findings is described. CT scan of the right knee showed features suggestive of combined ACL and PCL avulsion fractures. Arthroscopic findings showed that the injury was in fact a PCL avulsion fracture that was displaced anteriorly so as to mimic an ACL avulsion fracture on CT scan.
Avulsion fracture
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Posters [Publication Type]
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Ligaments
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Adjective Check List
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findings