Sjogren’s syndrome (SS) is an autoimmune disease affecting exocrine glands with known properties to cause chronic
systemic multi-organ disease involvement. It produced the typical features of sicca syndrome, but due to insidious
onset of the disease, patient may present with complications of the condition at the initial presentation. We present
a case of primary Sjogren’s syndrome (SS) who first presented with pulmonary manifestations and was subsequently
diagnosed as Lymphocytic Interstitial Pneumonia (LIP). The patient was extensively investigated and received appropriate treatment modalities.