This reports a case of dysembryoplastic neuroepithelial tumor (DNET) in a 5-year old male presenting with visual hallucination and seizures. Diagnostic workup revealed a homogenous cystic tumor located in the right temporo-parietal area which was considered as a low grade glioma. The patient underwent endoscopic third ventriculostomy with complete tumor excision and biopsy, revealing NET. Findings were confirmed by immunohistochemical staining with glial fibrillary action protein (GFAP), Alcian blue and synaptophysin. DNET is a recently described intracranial tumor under the World Health Organization classification of central nervous system (CNS) tumors. It is a unique entity of neuroglial tumors with excellent prognosis. Its worldwide incidence among all neuroepithelial tumors is 1.2% in patients under 20 years and 0.2% among patients over 20 years. This is the first case of DNET in the country as well as in our institution. Key points on the clinical manifestation, approach to diagnosis, distinctive radiologic and histopathologic characteristics, and management are discussed.
Neoplasms, Neuroepithelial

No abstract available.
Ganglioglioma* ; Neoplasms, Neuroepithelial ; Neuroblastoma ; Prognosis

No abstract available.
Magnetic Resonance Imaging* ; Neoplasms, Neuroepithelial*

No abstract available.
Magnetic Resonance Imaging* ; Neoplasms, Neuroepithelial*

Adult ; Female ; Humans ; Neoplasms, Neuroepithelial ; diagnosis

The authors presented one case of Dysembryoplastic neuroepithelial tumor revealed at a 23 years old woman with a 6 years epileptic. The histological and immunohistochemical aspect identified a “nonspecific” DNT. The authors discussed about the clinical, CT scanner, MRI and pathologic aspects and reviewed in literature
Neuroectodermal Tumors, Primitive, Peripheral ; Neoplasms, Neuroepithelial

Cerebral white matter tracts are altered by a brain tumor. We report a case of gliomatosis cerebri where the diffusion tensor fiber tract passes through the tumor.
Brain Neoplasms ; Diffusion Magnetic Resonance Imaging ; Diffusion* ; Neoplasms, Neuroepithelial*

Adult ; Humans ; Male ; Middle Aged ; Neoplasms, Neuroepithelial ; radiotherapy ; surgery

We report 2 cases of pediatric DNTs which presented with intractable seizures and no other associated neurologic abnormalities. They showed typical appearance of DNTs on neuroimaging and histopathology. Most patients with DNT can be cured by surgical treatment with exellent outcome and do not need ratio- or chemotheraphy. This study indicates that it is quite important to consider DNTs as one of differential diagnoses in patients with intractable seizures especially when they present only with seizures without other neurologic symptoms.
Child* ; Diagnosis, Differential ; Humans ; Neoplasms, Neuroepithelial* ; Neuroimaging ; Neurologic Manifestations ; Seizures*

No abstract available.
Magnetic Resonance Imaging* ; Magnetic Resonance Spectroscopy* ; Neoplasms, Neuroepithelial*