0.05). 6 cases of Hirschsprung′s disease showed microcolon with the appearances of shortage of colon frame, barium reflux into distal ileum and barium retention. Conclusion Local notch of the distal rectum, spiral or irregular bizarre saw-toothed contractions of the rectum and distal sigmoid colon, and delayed evacuation of barium are 3 valuable radiographic signs. Colitis itself isn′t a valuable diagnostic radiographic sign of Hirschsprung′s disease. It only shows inflammation of colon. And microcolon with the appearances of shortage of colon frame, barium reflux into distal ileum, and barium retention may suggest the diagnosis of total aganglionic colon.

Objective To analyze imaging findings of IPH and to study the correlation between the HRCT findings and the pulmonary function of IPH.Methods The information of 15 children with IPH were reviewed.Results The X-ray findings of IPH included ground glass opacity(n=9),exudative shadows(n=10),reticulonodular shadows(n=7),nodular shadows(n=6).The HRCT signs included abnormal bronchovascular bundles(n=12),ground glass opacity(n=12),exudative shadows ( n=11 ) ,disseminated micronodular shadows ( n=8 ) , thickened pulmonary lobular septa ( n=9 ) . The correlation between ground glass opacity and pulmonary function was 0.5394 ( P=0.134); The correlation between thickened pulmonary lobular septa and the pulmonary function was 0.9963(P=0.0001).Conclusion The HRCT examination is better than the X-ray examination. The positive correlation between thickened pulmonary lobular septa and pulmonary function change is significant,it is beneficial to estimate the damage of the palmonary.

Objective To study imaging features of Joubert syndrome on CT and MRI. Methods Ten cases with clinically diagnosed Joubert syndrome were retrospectively studied. Routine CT examinations were performed in all ten cases and MRI in four cases. Results He typical imaging features of Joubert syndrome included “midline cleft” between cerebellar hemispheres, “bat-wing” and “triangular-shaped” fourth ventricle, and “molar tooth sign”. On CT images, all cases had “midline cleft”, “bat-wing” and “triangular-shaped” fourth ventricle was present in nine cases, and “molar tooth sign” in eight cases. On MRI, “midline cleft”,“bat-wing” and “triangular-shaped” fourth ventricle , and “molar tooth sign” were present in all four cases. Conclusion There are typical imaging features of Joubert syndrome. CT and MRI play an important role for the diagnosis.

0.05).The differences were significant between the incidence of APCAs and the degree of pulmonary stenosis(P