1.Neonatal Pseudo-Bartter's Syndrome with Hypokalemia and ECG Changes Born to a Mother with Eating Disorder: A Case Report
Yuko AKUTSU ; Yuya HIGASHI ; Yukako NAGAYOSHI ; Manabu SUGIE ; Tsutomu KONDO ; Masatoshi IMAMURA
Journal of the Japanese Association of Rural Medicine 2017;66(2):153-158
It is essential to differentiate pseudo-Bartter's syndrome from Bartter's syndrome because both are accompanied by hypokalemia and metabolic alkalosis. In this study, we encountered a newborn girl with marked hypokalemia and metabolic alkalosis who was born vaginally at 41 weeks' gestation to a mother with pseudo-Bartter's syndrome and associated eating disorder. Venous blood gas analysis for transient respiratory distress revealed hypokalemia. Because hypokalemia did not improve, the newborn was transferred to our hospital 3 days after birth. Hema tological findings on admission showed serum potassium 2.6 mEq/L, bicarbonate 36.3 mmol/L, and base excess 12.8 mmol/L, with pH 7.56 and metabolic alkalosis. Electrocardiography (ECG) revealed sinus bradycardia as well as ST-segment depression, T-wave flattening, and prominent U-waves in all chest leads. Administration of enteral potassium began on postnatal day 5 but was terminated on postnatal day 7 because of rapid elevation of serum potassium, with consequent reversion of ECG abnormalities to age-appropriate levels. We later learned that the mother's serum potassium level was around 2 mEq/L because of the eating disorder, which frequently caused vomiting. Our findings suggest that this was a case of neonatal pseudo-Bartter's syndrome accompanied by severe electrolyte abnormalities and ECG changes due to maternal pseudo-Bartter's syndrome.
2.A Case of Replacement of the Ascending Aorta, Transverse Aortic Arch, Descending Aorta, and Upper Abdominal Aorta Using the "Elephant Trunk" Operation.
Norihiko Shiiya ; Keishu Yasuda ; Jun'ichi Oba ; Masatoshi Miyama ; Michiaki Imamura ; Tatsuzo Tanabe
Japanese Journal of Cardiovascular Surgery 1994;23(2):129-132
The“elephant trunk”operation, first described by Borst and associates, is a multistage operation for diffuse aneurysmal disease. We report a 59-year-old man complaining of hoarseness, who had a diffuse aneurysm extending from the ascending aorta to the upper abdominal aorta with occlusive disease in the neck branches. His aorta was replaced in two stages using the“elephant trunk”operation. The first stage operation, replacement of the ascending aorta and transverse aortic arch, was performed through a median sternotomy under selective cerebral perfusion. The second stage operation, replacement of the descending thoracic and upper abdominal aorta, was performed under F-F bypass. He had occlusive disease on bilateral carotid arteries with a history of brain infarction, had lost his left lower limb because of arteriosclerosis, and had undergone replacement of the infrarenal abdominal aorta because of an aneurysm. Despite a complicated preoperative general condition, the postoperative course was uneventful. The“elephant trunk” operation facilitates staged operation for diffuse aneurysmal disease as presented here, and thereby improves opeative result by reducing surgical stress.
3.Spontaneous Renal Artery Dissection: An Important Differential Diagnosis for Sudden Onset of Back Pain
Koshi Ota ; Eugene Kua ; Masatoshi Imamura ; HengJie Xu ; Masaaki Okutsu ; Takashi Kitao ; Naoko Takaoka
General Medicine 2013;14(2):126-129
Spontaneous renal artery dissection (SRAD) is uncommon and hence diagnosis is often delayed when ideally a quick one is preferred. We report a case of a 53 year-old male, with a known history of nephrolithiasis, who was admitted into hospital complaining of sudden onset left-sided back pain. Ultrasound showed a right-sided calculus instead of the expected left. A subsequent contrast computed tomography (CT) scan was done showing an infarcted segment of the left kidney. Further investigation with angiography and intravascular ultrasound (IVUS) revealed the presence of two left renal arteries with the distal originating left renal artery having dissected.