Extra-adrenal /retroperitoneal paraganglioma is a rare cause
of hypertension in young with increased incidence of
metastasis as compared to adrenal pheochromocytoma. We
present a case of a young female with history of headache,
nausea/vomiting, palpitations, uncontrolled hypertension,
heat intolerance and diaphoresis. The 24-hour urine
catecholamine levels were elevated. Clinical diagnosis of
pheochromocytoma was made and further evaluation with
Computed Tomography (CT) scan of the adrenals revealed
extradrenal para-aortic retroperitoneal mass in keeping with
paraganglioma. Gallium-68 DOTATE positron emission
tomography-CT scan (PET-CT) confirmed the diagnosis
without evidence of metastatic foci.
Paraganglioma