Cutis verticis gyrata is characterised by hypertrophy and folding of skin of scalp leading to gyrated appearance. Polan and Butterworth1 classified it into primary and secondary forms. Secondary CVG has been described with a wide variety of causes. Congenital melanocytic neavus appears to be the most common2. However it has been described with other naevoid abnormalities like Neavus lipomatoses, connective tissue nevi, genetic disorders such as neurofibromatoses, and endocrine disorders like acromegaly.