A 63-year-old man was admitted due to acute congestive heart failure. Transesophageal echocardiography demonstrated quadricuspid aortic valve malformation with concomitant severe aortic regurgitation. The valve was replaced by a 21mm Edward-MIRA and the postoperative course was uneventful. Although quadricuspid aortic valve is a rare anomaly, its potential for severe valve failure in adulthood should not be neglected.

A 47-year-old man suffered an idiopathic esophageal rupture and an emergency operation was performed. Postoperative CT revealed an aortic dissection at the level of the infra-renal aorta and the right common iliac artery. The maximum diameter of the aorta was 3.0cm, and that of the right common iliac artery was 2.5cm with a patent false lumen. The operation was done using the right extra-peritoneal approach. When the infra-renal aorta was clamped and opened, the false lumen was located on the right anterior wall of the aorta. There were 3 communicating holes presumably being the points of entry or re-entry. A bifurcation Dacron graft was put into the aorta and the bilateral iliac artery. His postoperative course was good and he was discharged on the 15th day after surgery. In this case, since the patient had no history of severe pain except for the time of esophageal rupture, the localized abdominal aortic dissection was suspected to have simultaneously occurred with the idiopathic esophageal rupture.

[Background] Surgical septal myectomy is the gold-standard therapy for hypertrophic obstructive cardiomyopathy (HOCM) in Europe and America. However, few cases underwent surgical septal myectomy in Japan. We have performed the surgical transaortic extended left ventricular myectomy (LV myectomy) as a first choice in HOCM patients unresponsive to pharmacologic therapy. We report the short and medium term clinical outcomes. Methods : From May 2012 to September 2014, 9 patients underwent extended LV myectomy without other accompanying procedures. All cases were symptomatic and peak left ventricular outflow tract pressure gradients (LVOTG) were 50 mmHg or more. We assessed clinical and echocardiographic outcomes at the short and medium term, intra-operative findings and cardiomyocyte pathological findings. Results : All patients (mean age 64.3 years, 56% female) underwent transaortic LV myectomy with no obvious complications. Postoperative LVOTG were controlled within 10 mmHg or less. SAM disappeared completely in all patients and MR decreased to mild or less. LVOTG sustained good control of 10 mmHg or less under low-dose dobutamine stress echocardiography at the medium term. Conclusion : Our transaortic extended LV myectomy procedure is effective in decreasing LVOTG, SAM and MR with low operative morbidity and mortality.

No abstract available.
Transcatheter Aortic Valve Replacement