Congenital intracranial tumors are rare and account for 0.5 to 1.5% of all childhood tumours. We report
a case of a 3 week old baby presenting with multi compartmental congenital intracranial immature
teratoma, fi rst of its kind in the literature. The child had gross total excision in two stages with aid of
neuronavigation. The short term outcome was good. The four years of follow-up with serial imaging
showed no tumour recurrence with a stable hydrocephalus after shunting. However, there is global
developmental delay with full time dependence of care giver