Neurofibromatosis type 1 (NF-1) is known to develop vascular lesions, yet they are uncommon. If missed or ignored, it can be limb-threatening. When a ruptured pseudoaneurysm is clinically identified, rapid surgical intervention is required. We discuss a case of NF-1 that involved a spontaneous rupture of the right deep brachial artery. A 41-year-old woman reported sudden right arm swelling and intensifying pain. She was hemodynamically stable; however, her right arm was enlarged and tense on examination. A radiological test revealed a deep brachial artery haemorrhage. The patient was promptly referred to a vascular surgeon and had endovascular intervention performed. Early detection, emergency angiography, and endovascular treatment for vascular lesions should be initiated immediately.
Neurofibromatoses