Transcatheter closure of rare type Ⅱ Abernethy malformation with pulmonary hypertension in children： A case report
10.3969/j.issn.1001-5256.2023.11.022
- VernacularTitle:介入封堵治疗小儿Ⅱ型Abernethy畸形合并肺动脉高压1例报告
- Author:
Heng ZHANG
1
;
Bin JIANG
2
;
Zhicheng FANG
1
;
Zhongji MENG
3
;
Enfu DU
4
Author Information
1. Department of Emergency Medicine, Hubei University of Medicine，Hubei Provincial Clinical Research Center for Precision Diagnosis and Treatment of Liver Cancer， Shiyan， Hubei 442000， China
2. Department of Hepatobiliary and Pancreatic Surgery，Hubei University of Medicine， Hubei Provincial Clinical Research Center for Precision Diagnosis and Treatment of Liver Cancer，Shiyan， Hubei 442000， China
3. Department of Infectious Diseases，Hubei University of Medicine， Hubei Provincial Clinical Research Center for Precision Diagnosis and Treatment of Liver Cancer，Shiyan， Hubei 442000， China
4. Department of Interventional Radiology， Taihe Hospital，Hubei University of Medicine， Hubei Provincial Clinical Research Center for Precision Diagnosis and Treatment of Liver Cancer， Shiyan， Hubei 442000， China
- Publication Type:Case Reports
- Keywords:
Abernethy Malformation;
Diagnosis;
Interventional Closure;
Management
- From:
Journal of Clinical Hepatology
2023;39(11):2663-2667
- CountryChina
- Language:Chinese
-
Abstract:
Abernethy malformation， also known as congenital portosystemic shunts， is rare in clinical practice， with less than 300 cases reported in the global literature up to 2019. The disease can have serious complications such as pulmonary hypertension， liver tumor， and liver failure and tends to have an extremely poor prognosis， and early diagnosis and active and effective treatment can reduce and delay the onset of complications. In this case， portography combined with balloon occlusion helped to display the underdeveloped slender portal vein with dysplasia， so that the child who was formerly misdiagnosed with type Ⅰ Abernethy malformation was diagnosed with type Ⅱ Abernethy malformation， and then the child was successfully treated by transcatheter closure. This article gives a detailed report of this case.
