A case of anti-neutrophil cytoplasmic antibodies-associated vasculitis with ocular masses as the main manifestation
10.3760/cma.j.cn441217-20220601-00602
- VernacularTitle:以眼部肿物为主要表现的抗中性粒细胞胞质抗体相关性血管炎1例
- Author:
Qijun LI
1
;
Shuangxin LIU
;
Qinghua YANG
;
Hong WANG
;
Lanying LI
;
Fangwei MO
;
Lu LYU
Author Information
1. 广东药科大学附属第一医院肾内科,广州 510080
- Keywords:
Anti-neutrophil cytoplasmic antibody-associated vasculitis;
Eye;
Granulomatosis with polyangiitis;
Ocular mass
- From:
Chinese Journal of Nephrology
2023;39(3):220-223
- CountryChina
- Language:Chinese
-
Abstract:
A case of anti-neutrophil cytoplasmic antibodies (ANCA)-associated vasculitis (AAV) with ocular masses as the main manifestation was reported. The patient was a middle-aged female, the initial symptom was eye swelling, pulmonary nodules were found before eye surgery, and further examination revealed proteinuria, hematuria and renal insufficiency. Renal pathology showed ANCA-associated glomerulonephritis. The final diagnosis was eye, kidney and lung lesions caused by AAV. Treatment with glucocorticoids and cyclophosphamide resulted in improvement in eye, kidney, and pulmonary lesions. Atypical clinical manifestations of AAV may lead to delayed diagnosis, and attention should be paid to the exclusion of AAV for ocular masses of unknown cause.