Surgical management of Dandy-Walker syndrome in infants and the literature review
10.3760/cma.j.cn101721-20220918-000424
- VernacularTitle:幼儿Dandy-Walker综合征外科处理所带来的思考及文献总结
- Author:
Xiaoqiang WANG
1
;
Jiru LI
;
Yunkun WANG
;
Hao XIA
;
Lili XING
;
Weiping WANG
Author Information
1. 上海交通大学医学院附属新华医院小儿神经外科，上海 200092
- Keywords:
Dandy-Walker syndrome;
Posterior fossa cyst;
Hydrocephalus;
Cystectomy;
Ventriculoperitoneal shunt
- From:
Clinical Medicine of China
2023;39(2):118-121
- CountryChina
- Language:Chinese
-
Abstract:
Dandy-Walker syndrome is one of the posterior fossa malformations, which is easily confused with arachnoid cyst or cerebellar dysplasia in clinical practice, leading to misdiagnosis. Dandy-Walker syndrome is easy to be combined with hydrocephalus, resulting in increased intracranial pressure, increased head circumference, growth retardation, spastic hemiplegia and other manifestations, and can also be accompanied by other nervous system malformations. On February 27, 2021, a child with Dandy-Walker syndrome with growth retardation as the primary manifestation was admitted to Xinhua Hospital Affiliated to Shanghai Jiaotong University School of Medicine. After multiple surgical treatment, the child's hydrocephalus was significantly improved. Through the analysis of the clinical data of the child's operation and the treatment of complications, it is helpful to improve the clinicians' understanding of the surgical treatment of the disease.
