Globus Pallidus Interna Deep Brain Stimulation for Chorea-Acanthocytosis.
10.3340/jkns.2015.57.2.143
- Author:
Jae Hyeok LEE
1
;
Won Ho CHO
;
Seung Heon CHA
;
Dong Wan KANG
Author Information
1. Department of Neurology, Pusan National University School of Medicine, Busan, Korea.
- Publication Type:Case Report
- Keywords:
Chorea-acanthocytosis;
Deep brain stimulation;
Chorea;
Globus pallidus
- MeSH:
Abetalipoproteinemia;
Chorea;
Deep Brain Stimulation*;
Drug Therapy;
Dyskinesias;
Globus Pallidus*;
Humans;
Neuroacanthocytosis*
- From:Journal of Korean Neurosurgical Society
2015;57(2):143-146
- CountryRepublic of Korea
- Language:English
-
Abstract:
Chorea-acanthocytosis (ChAc) is a rare hereditary disorder characterized by involuntary choreiform movements and erythrocytic acanthocytosis. Pharmacotherapy for control of involuntary movements has generally been of limited benefit. Deep brain stimulation (DBS) has recently been used for treatment of some refractory cases of ChAc. We report here on the effect of bilateral high-frequency DBS of globus pallidus interna in a patient with ChAc.