A Case of Klippel-Trenaunay Syndrome with Bilateral Nevus Flammeus in a Neonate.
- Author:
Kyu Chul HWANG
1
;
Sang Baik KIM
;
Sang Hyuk WOO
;
Il Hwan KIM
;
Dong Soo YU
Author Information
1. Department of Dermatology, College of Medicine, Korea University, Ansan, Korea. frank@hanafos.com
- Publication Type:Case Report
- Keywords:
Klippel-Trenaunay syndrome
- MeSH:
Capillaries;
Dermis;
Dilatation;
Extremities;
Humans;
Hypertrophy;
Infant, Newborn*;
Klippel-Trenaunay-Weber Syndrome*;
Lower Extremity;
Male;
Nevus*;
Parturition;
Port-Wine Stain*;
Skin;
Subcutaneous Fat;
Varicose Veins
- From:Korean Journal of Dermatology
2003;41(5):683-685
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
Klippel-Trenaunay syndrome is characterized as a triad of skin capillary malformations, varicose veins and venous malformations, and soft tissue hypertrophy of the affected extremity. Venous malformations are the main cutaneous manifestation of this syndrome, present at birth and are usually unilateral. The patient, a 3-day-old male neonate, was consulted to our clinic with the skin lesions of dark red to violaceous patches on both lower extremites and swelling on the right lower extremity. Histopathologically, a specimen from the dark violaceous skin of the right swollen extremity showed dilatation of capillaries of both dermis and subcutaneous fat. We present a case of Klippel-Trenaunay syndrome with the bilateral nevus flammeus of both lower extremities in a 3-day-old male neonate.