A case of moya-moya syndrome in mongolia
- VernacularTitle:“Мояа-мояа” хамшинжийн монгол дахь тохиолдол
- Author:
Baasanjav D
1
;
Ariunaa J
;
Oyun B
;
Boldbat R
;
Khandsuren B
;
Byambasuren TS
;
Amarjargal G
Author Information
1. Institute of Medical Science
- Publication Type:Review
- Keywords:
Moya-Moya syndrome;
stenosis of a.cerebri media;
catheter angiography;
duplex sonography;
- From:Mongolian Medical Sciences
2010;153(3):78-81
- CountryMongolia
- Language:Mongolian
-
Abstract:
In this published case of a male patient B., 53, has some epidemiological specifics. There is transient ischemic attack (TIA) syndrome, particularly while with clear mind there is sudden temporary paralysis of left leg and arm and loss of ability to speak. Temporary refers here to a period of 2-3 minutes after which everything gets back to normal. The incidence occurred again in two days during the medical treatment.MRA test concluded on the presence of obvious stenosis at the beginning part of both sides of a.cerebri media. The mentioned blood vessel pictures were undefined. Hence selected catheter angiography has been done with a purpose to establish the presence of a full occlusion or clogging stenosis in a.cerebri media and to clarify which specific vessels are being mobilized for the collateral supply. This test established that the a.cerebri media had full occlusion on both sides.A duplex sonography conducted in order to clarify characteristics of the clogging (blocking) process concluded the presence of gradual thickening of and blocking in intima (inner wall) of a. carotis interna. Based on these tests we considered that despite the atherosclerosis symptoms (Ischemia in ECG, 20 years of smoking,being male and aged 53, etc), this case had conditions of gradual (slow progressing) arteriopathy. Thus because of the presence in this case simultaneous arteriopathy process (gradually progressing and causing the blocking) in addition to atherosclerosis syndromes we consider it as a Moya-Moya syndrome. The disease of Moya-Moya is mostly found in children and youth and is a unique arteriopathy considered unrelated with atherosclerosis.
