A Case of Pneumatosis Cystoides Intestinalis in a Patient with Systemic Lupus Erythematosus.
- Author:
Jun Won PARK
1
;
Yeong Wook SONG
;
Ki Chul SHIN
Author Information
1. Department of Internal Medicine, Seoul National University College of Medicine, Seoul, Korea. kideb1@snu.ac.kr
- Publication Type:Case Report
- Keywords:
Pneumatosis cystoides intestinalis;
Lupus erythematosus, Systemic;
Prednisolone
- MeSH:
Female;
Humans;
Intestinal Mucosa;
Lupus Erythematosus, Systemic;
Middle Aged;
Myositis;
Pneumatosis Cystoides Intestinalis;
Prednisolone;
Prognosis;
Scleroderma, Systemic;
Vasculitis
- From:Korean Journal of Medicine
2012;83(2):283-286
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
Pneumatosis cystoides intestinalis, which is characterized by multiple air-filled cysts in the intestinal mucosa, submucosa, and subserosa, is associated with autoimmune disorders, including systemic sclerosis, inflammatory myopathy and, rarely, systemic lupus erythematosus (SLE). Here, we report the case of a 57-year-old female with a 2-year history of SLE who developed pneumatosis cystoides intestinalis. The patient's symptoms were improved with conservative management. Although pneumatosis cystoides intestinalis is an uncommon manifestation of SLE, and follows a mainly benign course, it can be associated with vasculitis, which has a poor prognosis.
