A Case of Incontinentia Pigmenti Associated with Ocular Complications.
- Author:
Hyun Kyung KOH
1
;
Chung Sook AHN
Author Information
1. Department of Ophthalmology, College of Medicine, Euha Womans University, Korea.
- Publication Type:Case Report
- MeSH:
Central Nervous System;
Female;
Humans;
Hyperpigmentation;
Incontinentia Pigmenti*;
Infant;
Skin Diseases;
Tooth
- From:Journal of the Korean Ophthalmological Society
1981;22(2):463-467
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
Incontinentia pigmenti is a hereditary anomaly characterized by hyperpigmentation in bizarre irregular patterns of striae, whorls, polyangular flecks, and fountains pray splatters. The dermatosis may be only a part of more generalized disorders which affect with great variability of the teeth, the eyes, the bones or central nervous system, or may be assotiated with other malformations or developmental disturbances. Recently, the authers have been experienced one case of incontinentia pigmenti which is assotiated with ocular complications in a 3 month old female and it was reviewed clinically with literatures.