Research advances in congenital extrahepatic portosystemic shunt
10.3969/j.issn.1001-5256.2023.02.032
- VernacularTitle:先天性肝外门体分流的研究进展
- Author:
Ying WANG
1
;
Shengrun XU
1
;
Di YU
1
;
Jinhui YANG
1
;
Jiang CHANG
1
Author Information
1. Department of Gastroenterology, The Second Affiliated Hospital of Kunming Medical University, Kunming 650101, China
- Publication Type:Review
- Keywords:
Congenital Extrahepatic Portosystemic Shunt;
Abernethy Malformation;
Diagnosis;
Therapeutics
- From:
Journal of Clinical Hepatology
2023;39(2):450-456
- CountryChina
- Language:Chinese
-
Abstract:
Congenital extrahepatic portosystemic shunt (CEPS) is also called Abernethy malformation, with the manifestation of congenital abnormal anastomosis between the portal vein and the inferior vena cava. CEPS is extremely rare in clinical practice and has diverse clinical symptoms, which often leads to missed diagnosis and misdiagnosis. This article reviews the pathogenesis, classification, clinical manifestation, diagnosis, and treatment of CEPS, so as to improve the awareness of this disease and provide a reference for further standardization of its diagnosis and treatment process in the future.
