Doege-Potter Syndrome: A presumptive case of Metastatic hemangiopericytoma with Persistent hypoglycemia in a 27-year-old male
https://doi.org/10.15605/jafes.036.01.16
- Author:
Von Lovel Zarra
1
;
Kenny Jun Demegillo
2
;
May Uyking-Naranjo
3
;
Ahmad Domado
1
Author Information
1. Department of Internal Medicine, Southern Philippines Medical Center, Davao City, Philippines
2. Section of Oncology, Department of Internal Medicine, Southern Philippines Medical Center, Davao City, Philippines
3. Section of Endocrinology, Department of Internal Medicine, Southern Philippines Medical Center, Davao City, Philippine
- Publication Type:Case Reports
- Keywords:
Doege-Potter syndrome
- MeSH:
Hemangiopericytoma;
Hypoglycemia
- From:
Journal of the ASEAN Federation of Endocrine Societies
2021;36(1):90-94
- CountryPhilippines
- Language:English
-
Abstract:
Doege-Potter syndrome (DPS) is a rare paraneoplastic condition characterized by hypoinsulinemic hypoglycemia from a solitary fibrous tumor. The underlying mechanism is the secretion of a prohormone form of insulin-like growth factor II (IGF-II) by the tumor, which causes decreased release of glucose into the circulation. We report the case of a 27-year-old Filipino male with presumptive DPS from a recurrent right temporo-zygomatic hemangiopericytoma (HPC). The complexity of DPS requires a multidisciplinary approach. Early screening for metastases from HPC may prevent the undesirable sequelae of the disease process.
- Full text:917-Article Text-13539-2-10-20210530.pdf