Rare presentation of right Adrenal Mass: Extramedullary haematopoiesis in a patient with Thalassaemia Intermedia
https://doi.org/10.15605/jafes.036.01.04
- Author:
Poh Shean Wong
1
;
Lit Sin Yong
1
;
Nor Afidah Binti Karim
1
;
Ee Leng Gan
2
;
See Guan Toh
2
;
Noor Lita Binti Adam
1
Author Information
1. Endocrinology Unit, Department of Medicine, Hospital Tuanku Jaafar Seremban, Malaysia
2. Haematology Unit, Department of Medicine, Hospital Tuanku Jaafar Seremban, Malaysia
- Publication Type:Case Reports
- Keywords:
Adrenal mass;
Adrenal incidentaloma;
Thalassaemia;
Congenital haemolytic disorder
- MeSH:
Hematopoiesis, Extramedullary
- From:
Journal of the ASEAN Federation of Endocrine Societies
2021;36(1):80-84
- CountryPhilippines
- Language:English
-
Abstract:
Extramedullary hematopoiesis (EMH) is a rare cause of adrenal mass. We present a 44-year-old woman who has thalassaemia intermedia, referred to Endocrinology clinic for huge adrenal mass. Along with a paraspinal lesion discovered in this patient, the leading diagnosis was EMH. The patient was treated with hypertransfusion and hydroxyurea, which led to a reduction in the size of the right adrenal mass and paraspinal mass. This case highlights the challenges in managing this rare condition. Although EMH is a rare cause of adrenal mass, the diagnosis must be considered in any patient with a history of a congenital hemolytic disorder, to avoid unnecessary surgical procedures.
- Full text:969-Article Text-13183-2-10-20210530.pdf
