Case report of lung transplantation for cystic fibrosis in a child
10.3760/cma.j.cn101070-20220120-00077
- VernacularTitle:肺移植治疗儿童囊性纤维化1例
- Author:
Baoying ZHENG
1
;
Ling CAO
Author Information
1. 首都儿科研究所附属儿童医院呼吸内科,北京 100020
- Keywords:
Cystic fibrosis;
Lung transplantation;
Child
- From:
Chinese Journal of Applied Clinical Pediatrics
2022;37(22):1718-1720
- CountryChina
- Language:Chinese
-
Abstract:
The clinical and genetic data of a child with cystic fibrosis who received double lung transplantation were retrospectively analyzed and related problems of cystic fibrosis lung transplantation were discussed.The child was diagnosed with cystic fibrosis in the Department of Respiratory, the Affiliated Children′s Hospital of Capital Institute of Pediatrics at the age of 6 years for the first time.The patient was hospitalized repeatedly for exacerbation of pulmonary infection, with no significant clinical improvement and progressive aggravation of malnutrition.In October 2019, the patient received double lung transplantation at the age of 17 years and 1 month.Two years after surgery, the clinical symptoms and quality of life have been notably improved, and no transplant-related complications were observed.Lung transplantation is an effective treatment for children with advanced cystic fibrosis lung disease.