Isolation of the Left Subclavian Artery with Right Aortic Arch in Association with Bilateral Ductus Arteriosus and Ventricular Septal Defect.
10.5090/kjtcs.2015.48.6.415
- Author:
Ji Seong LEE
1
;
Ji Young PARK
;
Seong Min KO
;
Dong Man SEO
Author Information
1. Department of Thoracic and Cardiovascular Surgery, Konkuk University Medical Center, Konkuk University School of Medicine, Korea. dmseo@kuh.ac.kr
- Publication Type:Case Report
- Keywords:
Aorta, arch;
Congenital heart disease;
Embryology
- MeSH:
Aorta, Thoracic*;
Arm;
Ductus Arteriosus*;
Embryology;
Heart Defects, Congenital;
Heart Septal Defects, Ventricular*;
Incidence;
Pulmonary Artery;
Subclavian Artery*;
Subclavian Steal Syndrome
- From:The Korean Journal of Thoracic and Cardiovascular Surgery
2015;48(6):415-418
- CountryRepublic of Korea
- Language:English
-
Abstract:
Right aortic arch with isolation of the left subclavian artery is a rare anomaly. The incidence of bilateral ductus arteriosus is sporadic, and a right aortic arch with isolation of the left subclavian artery in association with bilateral ductus arteriosus is therefore extremely rare. Since the symptoms and signs of isolation of the left subclavian artery can include the absence or underdevelopment of the left arm, subclavian steal syndrome, or pulmonary artery steal syndrome, the proper therapeutic approach is controversial. We report a case in which surgical reconstruction was used to treat isolation of the left subclavian artery with right aortic arch in association with bilateral ductus arteriosus and a ventricular septal defect.