Isolated Tricuspid Regurgitation: Initial Manifestation of Cardiac Amyloidosis.
10.5090/kjtcs.2015.48.6.422
- Author:
Dong Woog YOON
1
;
Byung Jo PARK
;
In Sook KIM
;
Dong Seop JEONG
Author Information
1. Department of Thoracic and Cardiovascular Surgery, Samsung Medical Center, Sungkyunkwan University School of Medicine, Korea. cabg.jeong@samsung.com
- Publication Type:Case Report
- Keywords:
Tricuspid valve;
Amyloidosis
- MeSH:
Adult;
Amyloidosis*;
Arrhythmias, Cardiac;
Cardiomyopathy, Restrictive;
Diagnosis;
Female;
Heart;
Humans;
Multiple Myeloma;
Plaque, Amyloid;
Tricuspid Valve;
Tricuspid Valve Insufficiency*
- From:The Korean Journal of Thoracic and Cardiovascular Surgery
2015;48(6):422-425
- CountryRepublic of Korea
- Language:English
-
Abstract:
Amyloid deposits in the heart are not exceptional in systemic amyloidosis. The clinical manifestations of cardiac amyloidosis may include restrictive cardiomyopathy, characterized by progressive diastolic and eventually systolic bi-ventricular dysfunction; arrhythmia; and conduction defects. To the best of our knowledge, no previous cases of isolated tricuspid regurgitation as the initial manifestation of cardiac amyloidosis have been reported. We describe a rare case of cardiac amyloidosis that initially presented with severe tricuspid regurgitation in a 42-year-old woman who was successfully treated with tricuspid valve replacement. Unusual surgical findings prompted additional evaluation that established a diagnosis of plasma cell myeloma.
