MRI in Movement Disorder Patients: "Hot cross bun" sign.
10.3348/jkrs.2003.49.2.85
- Author:
Seong Beom KOH
1
;
Byung Jo KIM
;
Min Kyu PARK
;
Kun Woo PARK
;
Nam Joon LEE
;
Dae Hie LEE
Author Information
1. Department of Neurology, Korea University College of Medicine. parkinson@naver.com
- Publication Type:Case Report
- Keywords:
Spinocerebellar ataxia;
Cerebellar hemorrhage
- MeSH:
Basal Ganglia Diseases;
Cerebellar Ataxia;
Diagnosis;
Hemorrhage;
Humans;
Magnetic Resonance Imaging*;
Movement Disorders*;
Multiple System Atrophy;
Parkinson Disease;
Spinocerebellar Ataxias
- From:Journal of the Korean Radiological Society
2003;49(2):85-88
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
Clinically, multiple system atrophy is difficult to differentiate from other basal ganglia disorders such as idiopathic Parkinson's disease or other types of cerebellar ataxia. The "hot cross bun"sign is a radiological sign which, it has been claimed, is highly specific for multiple system atrophy, and we describe four cases in which this sign occurred. In one patient, multiple system atrophy was clinically diagnosed, but in the other three, the respective clinical diagnosis was spinocerebellar ataxia type 1, type 2 (genetically), and old cerebellar hemorrhage. We therefore suggest that the hot cross bun sign reflects degeneration of transverse pontocerebellar fibers and is not a pathognomic sign of multiple system atrophy.
