Factor XI deficiency and orthognathic surgery: a case report on anesthesia management.
10.17245/jdapm.2015.15.1.25
- Author:
Soo Eon LEE
1
;
Yoon Ji CHOI
;
Seong In CHI
;
Hyun Jeong KIM
;
Kwang Suk SEO
Author Information
1. Department of Dental Anesthesiology, Seoul National University Dental Hospital, Seoul, Korea. stone90@snu.ac.kr
- Publication Type:Case Report
- Keywords:
Continuous noninvasive hemoglobin monitoring;
Factor XI deficiency;
Orthognathic surgery;
Rotation thromboelastometry
- MeSH:
Anesthesia*;
Factor XI Deficiency*;
Factor XI*;
Hemorrhage;
Humans;
Orthognathic Surgery*;
Osteotomy;
Thrombelastography
- From:Journal of Dental Anesthesia and Pain Medicine
2015;15(1):25-29
- CountryRepublic of Korea
- Language:English
-
Abstract:
Factor XI deficiency (Hemophilia C) is a very rare autosomal recessive bleeding disorder. Patients with factor XI deficiency do not typically show any spontaneous bleeding or specific symptoms. Sometimes those who have this disorder are identified during special situations such as trauma or surgery. Orthognathic surgery is particularly associated with a high bleeding risk. Therefore, great care must be taken when treating patients with bleeding disorders such as factor XI deficiency. There are a few reports that address the management of patients with bleeding disorders during orthognathic surgery. The current report describes a patient with factor XI deficiency who underwent Le Fort I osteotomy together with bilateral sagittal split osteotomy. The patient's condition was assessed using both rotation thromboelastometry (ROTEM™) and noninvasive measurements of total hemoglobin (SpHb) using Masimo Radical 7 (Masimo Co. CA, USA).
