Immunoglobulin G4 Non-Related Sclerosing Disease with Intracardiac Mass Mimicking Mitral Stenosis: Case Report.
10.3346/jkms.2013.28.12.1830
- Author:
Ji Won HWANG
1
;
Sung Ji PARK
;
Hye Bin GWAG
;
Jung Min HA
;
Woo Joo LEE
;
Eun KIM
;
Sehyo YUNE
;
Jung Sun KIM
;
Yang Jin PARK
;
Duk Kyung KIM
Author Information
1. Department of Internal Medicine, Samsung Medical Center, Sungkyunkwan University School of Medicine, Seoul, Korea.
- Publication Type:Case Reports
- Keywords:
Immunoglobulin G4 Non-Related Sclerosing Disease;
Periaortitis;
Left Atrium Mass;
Mitral Valve Stenosis
- MeSH:
Aged;
Aorta, Abdominal/pathology;
Diagnosis, Differential;
Echocardiography;
Female;
Humans;
Immunoglobulin G/*blood/immunology;
Magnetic Resonance Imaging;
Mitral Valve Stenosis/diagnosis;
Myocardium/*pathology;
Peritoneum/surgery;
Positron-Emission Tomography;
Retroperitoneal Fibrosis/*congenital/diagnosis/drug therapy/ultrasonography;
Steroids/therapeutic use;
Tomography, X-Ray Computed
- From:Journal of Korean Medical Science
2013;28(12):1830-1834
- CountryRepublic of Korea
- Language:English
-
Abstract:
The cardiovascular system may be one of the target organs of both immunoglobulin G4 related and non-related systemic multifocal fibrosclerosis. We present a case of IgG4 non-related systemic multifocal fibrosclerosis mimicking mitral stenosis on echocardiography. For a more detailed differential diagnosis, we used multimodal imaging techniques. After surgical biopsy around the abdominal aortic area in the retroperitoneum, histological examination revealed IgG4 non-related systemic multifocal fibrosclerosis. We describe the multimodal imaging used to diagnose IgG4 non-related systemic multifocal fibrosclerosis and a positive response to steroid treatment. There have been no previous case reports of IgG4 non-related systemic multifocal fibrosclerosis with intracardiac involvement. Here, we report a case of IgG4 non-related systemic multifocal fibrosclerosis mimicking mitral stenosis.
