Two Cases of Herlyn-Werner-Wunderlich Syndrome
10.13104/imri.2022.26.3.166
- Author:
Yuri KIM
1
;
Young Mi KU
;
Yoo Dong WON
Author Information
1. Department of Radiology, College of Medicine, The Catholic University of Korea, Seoul, Korea
- Publication Type:Case Report
- From:Investigative Magnetic Resonance Imaging
2022;26(3):166-170
- CountryRepublic of Korea
- Language:English
-
Abstract:
Herlyn-Werner-Wunderlich (HWW) syndrome—also known as obstructed hemivagina and ipsilateral renal anomaly—is a rare congenital anomaly of Müllerian ducts and Wolffian ducts which is classically characterized by uterine didelphys, obstructed hemivagina, and ipsilateral renal agenesis; however, there are various combinations of uterine anomalies, obstruction sites, and renal anomalies that can occur as anatomic variants of HWW syndrome. Most patients show symptoms of recurrent lower abdominal pain or pelvic mass after the onset of menarche. Diagnosis can be delayed due to regular menstruation through non-obstructed hemivagina, which can lead to complications such as endometriosis, pyocolpos, pelvic inflammatory disease, and infertility. Here, we report two cases of females who presented dysmenorrhea and pelvic mass after the onset of puberty and were diagnosed with HWW syndrome through pelvic MRI. A review of the relevant literature was also provided.
