Incomplete Form of Shone Complex in an Adult Congenital Heart Disease Patient
10.5090/kjtcs.2019.52.2.100
- Author:
Beatrice Chia Hui SHIH
1
;
Jae Hong LIM
;
Jooncheol MIN
;
Eung Re KIM
;
Jae Gun KWAK
;
Woong Han KIM
Author Information
1. Department of Pediatric Thoracic and Cardiovascular Surgery, Seoul National University Children’s Hospital, Seoul National University College of Medicine, Seoul, Korea. woonghan@snu.ac.kr
- Publication Type:Case Report
- From:The Korean Journal of Thoracic and Cardiovascular Surgery
2019;52(2):100-104
- CountryRepublic of Korea
- Language:English
-
Abstract:
Shone complex is a rare congenital disorder that involves 4 obstructive lesions of the left heart, as follows: parachute mitral valve, supravalvular mitral ring, subaortic stenosis, and coarctation of the aorta. Incomplete forms with 2 or 3 of these lesions in adult patients have been rarely reported in the literature, meaning that insufficient general data exist concerning the surgical strategy and clinical follow-up. Herein, we report the case of a 31-year-old woman with a diagnosis of incomplete form of Shone complex with parachute mitral valve and coarctation of the aorta who underwent successful single-stage surgical repair.
