Sporadic Creutzfeldt-Jakob disease
10.3760/cma.j.cn113694-20211228-00930
- VernacularTitle:散发性克-雅病
- Author:
Jiatang ZHANG
1
;
Yuheng SHAN
Author Information
1. 解放军总医院神经内科医学部,北京100853
- Keywords:
Creutzfeldt-Jakob disease, sporadic;
Diagnosis;
Auxiliary examination
- From:
Chinese Journal of Neurology
2022;55(4):363-371
- CountryChina
- Language:Chinese
-
Abstract:
Sporadic Creutzfeldt-Jakob disease is a rare condition with a rapid disease course and a mortality rate of 100%. In clinical practice, it is difficult to diagnose, even if consistent conventional laboratory methodologies are used. This article will give a summary on the epidemiology, pathogenesis, clinical manifestations, auxiliary examination, diagnosis and differential diagnosis, management, and prognosis of sporadic Creutzfeldt-Jakob disease.