A Case of Disseminated Pagetoid Reticulosis.
- Author:
Hyeong Jin CHON
1
;
Ji Soo PARK
;
Sook Ja SON
;
Dong Jun KIM
Author Information
1. Department of Dermatology, National Medical Center, Seoul, Korea.
- Publication Type:Case Report
- Keywords:
Pagetoid reticulosis;
Disseminated;
CD30+
- MeSH:
Aged;
Buttocks;
Epidermis;
Female;
Humans;
Lower Extremity;
Lymphoproliferative Disorders;
Pagetoid Reticulosis*;
Thorax
- From:Korean Journal of Dermatology
2000;38(6):802-805
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
Pagetoid reticulosis(PR) is a rare lymphoproliferative disorder that has been divided into the localized and disseminated type. There has been ongoing debate about the nature of PR. Some authors have regarded PR as a variant of mycosis fungoides(MF). However recent reported cases suggest that PR may represent a spectrum of lymphoproliferative disorders that may not be related to MF. We report a case of a 65-year-old woman who had an erythematous plaque on the anterior chest, buttock and lower extremities for 2 years. Histologically there was dense infiltrate of predominantly CD8-/CD30+ atypical mononuclear cells in the epidermis that produce a pagetoid appearance. We believe this is the first reported case of disseminated pagetoid reticulosis in the Korean literature.