A Case of Gronblad-Strandberg Syndrome with Subretinal Neovascularization.
- Author:
Sung Gi CHO
1
;
Dong Eul SHIN
;
Jae Sun LEE
Author Information
1. Department of Ophthalmology, Korea Veterans Hospital, 6-2
- Publication Type:Case Report
- Keywords:
angioid streak;
pseudoxanthoma elasticum;
subretinal neovascularization
- MeSH:
Angioid Streaks;
Atrophy;
Cardiovascular System;
Dermis;
Elastic Tissue;
Female;
Humans;
Middle Aged;
Pseudoxanthoma Elasticum*
- From:Journal of the Korean Ophthalmological Society
1989;30(5):835-838
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
The authors experienced one case of Gronblad-Strandberg syndrome with subretinal neovascularization which showed characteristic signs of pseudoxanthoma elasticum(PXE) and angioid streak. PXE is an uncommon hereditary disorder which involves the elastic tissue of the dermis and may also involve the eye and the cardiovascular system. Angioid streaks are red or dark-brown jagged irregular lines extending in spoke like fashion toward periphery from an area of peripapillary atrophy. We report a case of Gronblad-Strandberg syndrome with subretinal neovasculari zation in a 49 year old korean female.