A Case of Thoracic Endovascular Aortic Repair for Subacute Aortic Dissection Stanford Type B in a Patient with Marfan Syndrome
- VernacularTitle:B型大動脈解離亜急性期に TEVAR を行い3年後に胸腹部置換追加を要したマルファン症候群の1例
- Author:
Shun NAKAJI
1
;
Takashi MIURA
1
;
Ichiro MATSUMARU
1
;
Akihiko TANIGAWA
1
;
Yutaro KAWAGUCHI
1
;
Shunsuke TAGUCHI
1
;
Yugo MURAKAMI
1
;
Kikuko OBASE
1
;
Kiyoyuki EISHI
1
;
Shinichiro TANIGUCHI
2
Author Information
- Keywords: Marfan syndrome; aortic dissection; endovascular therapy; TEVAR
- From:Japanese Journal of Cardiovascular Surgery 2022;51(1):48-52
- CountryJapan
- Language:Japanese
- Abstract: A 41-years-old man with Marfan syndrome developed acute aortic dissection Stanford Type B. A new entry was located at the distal aortic arch. Medical treatment was given for a month, but the proximal descending aorta expanded to 50 mm. Because he had undergone partial arch replacement at the age of 36, thoracic endovascular aortic repair (TEVAR) using the synthetic graft as proximal landing zone was performed to close the entry. Six months after TEVAR, the false lumen around the stent graft disappeared. Distal stent graft-induced new entry (d-SINE) did not occur after TEVAR. Three years after TEVAR, we performed thoracoabdominal aortic replacement because of expansion of the residual false lumen without any complication. Endovascular therapy could be useful option for extensive aortic lesion even in Marfan syndrome.
