Peutz-Jeghers Syndrome Associated with Jejuno- jenunal Intussusception.
- Author:
Min Sung AN
1
;
Woon Won KIM
;
Sang Hoon OH
;
Nan Joo LEE
Author Information
1. Department of Surgery, Dongnae Paik Hospital, Busan, Korea. drkww@lycos.co.kr
- Publication Type:Case Report
- Keywords:
Peutz-Jeghers syndrome;
Intussusception
- MeSH:
Abdominal Pain;
Female;
Gastrointestinal Tract;
Genetic Diseases, Inborn;
Hemorrhage;
Humans;
Intestinal Obstruction;
Intussusception;
Peutz-Jeghers Syndrome;
Pigmentation;
Polyps;
Skin;
Stress, Psychological
- From:Journal of the Korean Surgical Society
2008;74(5):383-386
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
Peutz-Jeghers syndrome (PJS) is a rare hereditary disease where the clinical manifestations are multiple harmatomatous gastrointestinal polyps and pigmentations of the skin. A harmatomatous polyp can develop at any part of the gastrointestinal tract, and the proximal small bowel is frequently involved. Intestinal obstruction, bleeding and intussusception, caused by GI polyps have been reported, which often require repeated surgery. A female patient presented with suffering of abdominal pain for two days duration. The patient was diagnosed with intussusception, and a resection and anastomosis of the small bowel was performed. The patient was treated for 15 days, and was discharged from the hospital without any particular complications. We report this case with a review of the literature.
