A Rare Case of Granulomatosis with Polyangiitis-Related Periaortitis at the Ascending Aorta
10.3348/jksr.2019.80.3.537
- Author:
Sang Hyup HONG
1
;
Gil Sun HONG
;
Choong Wook LEE
;
Gi Hong KIM
Author Information
1. Department of Radiology and Research Institute of Radiology, University of Ulsan College of Medicine, Asan Medical Center, Seoul, Korea. gshong@amc.seoul.kr
- Publication Type:Case Report
- From:Journal of the Korean Radiological Society
2019;80(3):537-542
- CountryRepublic of Korea
- Language:English
-
Abstract:
Acute aortic syndrome including intramural hematoma is a life-threatening disease encountered in the emergency department with high in-hospital mortality even when a timely diagnosis is made. Therefore, accurate differential diagnosis of acute aortic syndrome and its mimics is important to determine the patient's treatment plan. Until now, a few pathologic diseases mimicking aortic intramural hematoma such as periaortic lymphoma and immunoglobulin G4-elated periaoritis have been reported. Here, we report a rare case of granulomatosis with polyangiitis-related periaortitis misdiagnosed as aortic intramural hematoma presenting to the emergency department with chest pain and similar radiologic findings.
