A Case of Malignant Peripheral Nerve Sheath Tumor in Neurofibromatosis.
- Author:
Ji Ho LEE
1
;
Chul Jong PARK
;
Jong Yuk YI
;
Jung Soo KIM
;
Hae Myung JEON
Author Information
1. Department of Dermatology, College of Medicine, The Catholic University of Korea, Seoul, Korea.
- Publication Type:Case Report
- Keywords:
Malignant peripheral nerve sheath tumor;
Neurofibromatosis
- MeSH:
Adult;
Breast;
Cafe-au-Lait Spots;
Female;
Humans;
Neoplasm Metastasis;
Neurofibroma;
Neurofibromatoses*;
Neurofibromatosis 1;
Peripheral Nerves*
- From:Korean Journal of Dermatology
1999;37(10):1535-1537
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
Malignant peripheral nerve sheath tumor is a neoplasm that most often arises in anatomically discernible peripheral nerves or neurofibroma. A 37-year-old woman presented with a rapid growing pedunculated, huge mass on the left breast for 1 month. She has suffered from neurofibromatosis type 1 with multiple cafe au lait spots and neurofibromas. The huge mass has developed from a subcutaneous nodule on the left breast. The clinical and histopathological data showed a malignant peripheral nerve sheath tumor. Since no sign of the metastasis was observed, local excision was performed. We, herein, report a case of malignant peripheral nerve sheath tumor developed in the patient of nurofibromatosis type 1.
