Left Pulmonary Artery Agenesis Accompanied with Fistula of Left Circumplex Artery to Left Bronchial Artery.
10.4070/kcj.2003.33.10.928
- Author:
Dong Yang PARK
1
;
Nam Ho LEE
;
Seung Hyuk CHOI
;
In Sang YUN
;
Kwang Hyuk PARK
;
Chul Sung JUNG
;
Jin Suk KO
;
Dae Ik NAM
;
Dae Sung KIM
;
Chi Hyun CHOI
;
Kwun Woo HAN
Author Information
1. Department of Internal Medicine, College of Medicine, Hallym University, Seoul, Korea. namholee@hanmail.net
- Publication Type:Case Report
- Keywords:
Pulmonary artery agenesis;
Coronary arterial fistula
- MeSH:
Aorta, Thoracic;
Arteries*;
Bronchial Arteries*;
Coronary Angiography;
Coronary Vessels;
Ductus Arteriosus, Patent;
Fistula*;
Heart Septal Defects, Ventricular;
Hemoptysis;
Humans;
Lung;
Pulmonary Artery*;
Respiratory Tract Infections;
Tetralogy of Fallot;
Tomography, X-Ray Computed
- From:Korean Circulation Journal
2003;33(10):928-932
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
Left pulmonary artery agenesis, accompanied by a coronary arterial fistula, is a very rare anomaly. Although unilateral pulmonary artery agenesis is associated with other cardiovascular defects, like as ventricular septal defect, patent ductus arteriosus, and tetralogy of fallot, this anomaly, accompanied by a coronary arterial fistula, has not yet been reported. Most patients with no associated cardiac anomalies have only minor, or absent, symptoms, and survive to adulthood, but some patients may suffer from recurrent respiratory infections and hemoptysis. The vessel to the affected lung in many of the proved cases has been described as arising from either the bronchial artery or the aortic arch. The blood supply from the coronary artery to the affected lung has never been reported. Recently, a case of left pulmonary artery agenesis, accompanied with a coronary arterial fistula was experienced, which was diagnosed by coronary angiography and a chest CT, which is presented, with the review of relevant literature.
