Histiocytosis X Case Report.
- Author:
Chun Sik CHOI
1
;
Kyong Sik PARK
;
Ki Yong PARK
;
Mun Bae JU
Author Information
1. Department of Neurosurgery, Korea General Hospital, Seoul, Korea.
- Publication Type:Original Article
- MeSH:
Child, Preschool;
Curettage;
Eosinophilic Granuloma;
Exophthalmos;
Histiocytosis*;
Histiocytosis, Langerhans-Cell*;
Humans;
Male;
Polyuria;
Rabeprazole;
Young Adult
- From:Journal of Korean Neurosurgical Society
1981;10(1):341-346
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
Eosinophilic granuloma, Hand-Schuller-Christian and Abt-Letterer-Siewe syndrome are known to be the same disease entity involving the reticulohistiocytic system of the body, although their clinical manifestations are different. So they were included under the term of Histiocytosis X and this concept has been generally accepted. The authors have experienced one case of Hand-Schuller-Christian disease and that of eosinophilic granuloma. The former was a 23 years old man with complaints of exophthalmos, polyuria and a tender palpable mass on the right parietal area and in the latter a soft pulastile mase located on the left parietal area in a 3 year old boy. There was no neurological deficits on their admission. We managed them with radiation and steroid therapy following surgical curettage.
