A Case of Multifocal Fibrosclerosis with CNS Involvement.
- Author:
Kye Hoon LEE
1
;
Jae Kwan CHA
;
Ju Han KIM
;
Kyung Cheon CHUNG
;
Jong Cheol RHEE
Author Information
1. Department of Neurology, Hanyang University, Korea.
- Publication Type:Case Report
- MeSH:
Cholangitis, Sclerosing;
Fibrosis;
Humans;
Meningitis;
Middle Aged;
Orbit;
Orbital Pseudotumor;
Retroperitoneal Fibrosis;
Thyroid Gland;
Thyroiditis;
Vasculitis, Central Nervous System
- From:Journal of the Korean Neurological Association
1990;8(2):372-377
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
Multifocal fibrosclerosis, a rare disorder, has no known etiology and is considered to be a systemic illness manifested by combinations of fibrosing process of multiple areas such as mediastinal fibrosis, retroperitoneal fibrosis, orbital pseudotumor, sclerosing cholangitis, and Reidel's thyroiditis. We have experienced a 49-year-old man with pseudotumor of the orbit, sclerosing cholangitis, and CNS involvements included unrecognized meningitis and suspicious CNS vasculitis. The patient showed clinical improvement with corticosteroid therapy.
