Two Families of Diunally Fluctuating Hereditary Progressive Dystonia.
- Author:
Jae Woo KIM
1
;
Gyu Sup CHO
;
Ho Jin MYUNG
Author Information
1. Department of Neurology, Dong-A University, Korea.
- Publication Type:Case Report
- MeSH:
Dystonia*;
Female;
Gait;
Humans;
Levodopa;
Movement Disorders
- From:Journal of the Korean Neurological Association
1990;8(2):389-392
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
Diurnally fluctuating hereditary progessive dystonia is a rare movement disorder characterized by marked diurnal fluctuation of symptoms and dramatic response to levodopa. We report two advanced female patients of two families who presented with progressive dystonia and gait disturbance. Both patients have a family history and showed excellent response to levodopa.
