Lymphocytic interstitial pneumonia in a patient with Sjögren's syndrome.
10.12701/yujm.2016.33.2.112
- Author:
Eun Hye LEE
1
;
Ji Eun PARK
;
Eun Kyong GOAG
;
Young Joo KIM
;
In Young JUNG
;
Chi Young KIM
;
Young Mok PARK
;
Jung Mo LEE
;
Moo Suk PARK
Author Information
1. Division of Pulmonology, Department of Internal Medicine, Yonsei University College of Medicine, Seoul, Korea. PMS70@yuhs.ac
- Publication Type:Case Report
- Keywords:
Lymphocytic interstitial pneumonia;
Sjögren's syndrome
- MeSH:
Adrenal Cortex Hormones;
Adult;
Biopsy;
Connective Tissue;
Dyspnea;
Female;
Humans;
Immune System;
Immunosuppressive Agents;
Lip;
Lung Diseases, Interstitial*;
Lymphocytes;
Lymphoproliferative Disorders;
Mouth;
Plasma Cells;
Steroids
- From:Yeungnam University Journal of Medicine
2016;33(2):112-115
- CountryRepublic of Korea
- Language:English
-
Abstract:
Lymphocytic interstitial pneumonia (LIP) is a rare benign lymphoproliferative disorder characterized by diffuse infiltration of the pulmonary parenchymal interstitium by polyclonal lymphocytes and plasma cells. LIP has been associated with a variety of clinical conditions; such as connective tissue disorders and other immune system abnormalities. Treatment usually involves administration of corticosteroids and other immunosuppressants. We report on a 38-year-old female patient who complained of shortness of breath, dry mouth, and dry eyes for more than 1 month, and was positive for Raynaud's phenomenon. Based on surgical biopsy, she was diagnosed as having LIP accompanied by Sjögren's syndrome. The patient was treated with high-dose steroids followed by maintenance therapy for approximately 2 years, and her condition improved.
