Dietary management of one child with glycogen storage disease type I and severe hyperlipidemia
10.3760/cma.j.cn211501-20201026-04303
- VernacularTitle:一例I型糖原累积症伴严重高脂血症患儿的饮食管理
- Author:
Lin YUAN
1
;
Zhengqing QIU
;
Rongrong LI
;
Jing SUN
;
Yang LI
Author Information
1. 北京协和医学院护理学院 100144
- Keywords:
Glycogen storage disease type I;
Severe hyperlipidemia;
Dietary management
- From:
Chinese Journal of Practical Nursing
2021;37(17):1351-1355
- CountryChina
- Language:Chinese
-
Abstract:
Objective:To summarizes the diet management of one child with GSD I and severe hyperlipidemia.Methods:Key points of diet management include: making an individual diet plan, correcting parents' dietary misunderstanding, adjusting dietary and keeping following up regularly and keeping a food diary.Results:Following up for 11 months, the children basically formed a stable diet pattern, the blood glucose level was basically maintained between 4~6 mmol/L, the indicators of hyperlipidemia, hyperlactic acid and liver function were significantly improved compared with the previous period, and the height increase was guaranteed, while the weight gain was effectively controlled.Conclusions:It shows that individualized dietary guidance has a significant effect on the maintenance of blood glucose level, improvement of growth and development status and metabolic control in children with GSD I.
