Case report of bronchial Dieulafoy disease in children
10.3760/cma.j.cn101070-20200312-00385
- VernacularTitle:儿童支气管Dieulafoy病1例
- Author:
Feng HAN
1
;
Qing DU
;
Xiaoxia LU
;
Yanli WANG
;
Peng CHEN
;
Sijing LIU
;
Xinxian LIU
Author Information
1. 华中科技大学同济医学院附属武汉儿童医院呼吸内科，武汉 430016
- Keywords:
Child;
Hemoptysis;
Bronchoscopy;
Bronchial Dieulafoy
- From:
Chinese Journal of Applied Clinical Pediatrics
2021;36(15):1191-1193
- CountryChina
- Language:Chinese
-
Abstract:
The clinical data of a child with bronchial Dieulafoy disease treated in Wuhan Children′s Hospital Affiliated to Tongji Medical College, Huazhong University of Science and Technology, was analyzed retrospectively.The patient was a 9-month-old boy, who was admitted to hospital due to " intermittent hematemesis vomiting blood for 6 hours" . Chest CT suggested ground-glass opacity in both lungs.Electronic bronchoscopy showed that the neoplasm bulged into the lumen at the opening of the right inferior lobar bronchus, and fresh blood oozed from the basal segment of the neoplasm during the operation.Bronchial arteriography and transcatheter bronchial artery embolization were performed due to recurrent hemoptysis, during which the patient was diagnosed with bronchial arterial vascular malformation and finally diagnosed with bronchial Dieulafoy disease after consulting the relevant literatures.The disease is infrequent and characterized by rupture hemorrhage of bronchial submucosal malformed artery, the etiology and pathogenesis of which are still unclear, and it may be related to congenital vascular malformation in children.Bronchoscopy for hemoptysis of unknown cause in children should be performed with caution.If small and smooth protruded nodular lesions are seen under the bronchoscope, the bronchial Dieulafoy disease should be considered, and the lesions should not be touched too much or subjected to biopsy blindly.Fatal massive hemorrhage can be avoided by bronchial arteriography and bronchial artery embolization.
