MRI Findings of Obstructed Hemivagina and Ipsilateral Renal Agenesis (OHVIRA syndrome) with a Blind Megaureter: Case Report.
10.13104/imri.2015.19.3.196
- Author:
Yun Hee CHO
1
;
Deuk Jae SUNG
;
Na Yeon HAN
;
Beom Jin PARK
;
Min Ju KIM
;
Ki Choon SIM
;
Sung Bum CHO
Author Information
1. Department of Radiology, Korea University Anam Hospital, College of Medicine, Korea University, Seoul, Korea. urorad@korea.ac.kr
- Publication Type:Case Report
- Keywords:
Mullerian duct anomaly;
Renal anomaly;
Blind megaureter;
Magnetic resonance imaging (MRI)
- MeSH:
Abdominal Pain;
Adolescent;
Congenital Abnormalities;
Drainage;
Female;
Humans;
Hysterectomy;
Magnetic Resonance Imaging*;
Urinary Bladder
- From:Investigative Magnetic Resonance Imaging
2015;19(3):196-199
- CountryRepublic of Korea
- Language:English
-
Abstract:
Obstructed hemivagina and ipsilateral renal anomaly (OHVIRA) syndrome is an uncommon congenital abnormality of the female urogenital tract characterized by the triad of uterine didelphys, obstructed hemivagina, and ipsilateral renal agenesis. A 13-year-old female presented with acute lower abdominal pain. Magnetic resonance imaging (MRI) revealed uterine didelphys, hematometrocolpos, obstructed hemivagina, and right ipsilateral agenesis, consistent with OHVIRA syndrome. Also, a well-defined mass with fluid signal intensity, mimicking adnexal neoplasm was seen in the right lower pelvic cavity adjacent to the posterior wall of the bladder. Vaginal septotomy and drainage of hematometrocolpos were done initially, but unilateral hysterectomy was later performed to relieve the patient's symptoms. The cystic mass in the right lower pelvic cavity was also excised and confirmed as a blind megaureter.
