Unusual Manifestation of Immunoglobulin G4-Related Disease Involving the Retroperitoneum:A Case Report
- Author:
Byungsoo KIM
1
;
Jung Wook SEO
Author Information
- Publication Type:Case Report
- From:Journal of the Korean Radiological Society 2021;82(2):487-492
- CountryRepublic of Korea
- Language:English
- Abstract: Immunoglobulin G4 (IgG4)-related disease is a systemic disease characterized by dense lymphoplasmacytic infiltrates with abundant IgG4-positive plasma cells and fibroblast proliferation. The retroperitoneal involvement of IgG4-related disease usually appears as a soft-tissue mass covering the abdominal aorta or entrapping the ureters, resulting in hydronephrosis. Here, we present a case of IgG4-related disease with retroperitoneal involvement in a 75-yearold woman with an unusual manifestation. A preoperative computed tomography (CT) scan revealed an irregular infiltrative retroperitoneal mass invading the normal anatomic barriers, raising the suspicion of malignancy or inflammation. Contrast-enhanced CT revealed a homogeneous progressive enhancement of the mass.
