Idiopathic Familial Intracerebral Calcification with Pyramidal Tract Degeneration.
- Author:
Young Chul CHOI
1
;
Young Ho SOHN
;
Yoon Joong KIM
;
Jae Woo JUNG
;
Jin Soo KIM
;
Youn Mee HWANG
Author Information
1. Department of Neurology, Yonsei University, Korea.
- Publication Type:Case Report
- MeSH:
Bulbar Palsy, Progressive;
Humans;
Magnetic Resonance Imaging;
Male;
Muscle Spasticity;
Pyramidal Tracts*;
Quadriplegia
- From:Journal of the Korean Neurological Association
1991;9(1):101-106
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
A l9-year-old boy was admitted because of progressive spastic quadriparesis and bulbar palsy which developed from 3 years ago. The results of all performed laboratory tests were normal, but neuroradiologic tests revealed intracerebral calcification and degeneration of oilateral pyramidal tracts. Idiopathic familial intracerebral calcification was rarely occurred and presented usually with various extrapyramidal and cortical symptoms. Mild pyramidal symptoms were also associated in some reported cases, but none of them showed predominant spasticity as well as suspicious pyramidal tract degeneration on magnetic resonance imaging.
