Osteosarcomatous Transformation in Mazabraud Syndrome: A Case Report
- Author:
Yang Il PARK
1
;
Ji Young YOO
;
Joon Seog KONG
Author Information
- Publication Type:Case Report
- From:Journal of the Korean Radiological Society 2021;82(5):1346-1351
- CountryRepublic of Korea
- Language:English
- Abstract: Mazabraud syndrome is a rare benign disease that is accompanied by polyostotic fibrous dysplasia and intramuscular myxoma. Malignant transformation of fibrous dysplasia occurs in approximately 1% of cases. To date, only eight cases of malignant transformation, of fibrous dysplasia to osteosarcoma, in Mazabraud syndrome have been reported worldwide. The authors report the first case of osteosarcomatous transformation in a patient with Mazabraud syndrome in the Republic of Korea, focusing on imaging findings.
