Spinal Dysraphism and Tethered Cord Syndrome.
10.5124/jkma.2009.52.1.78
- Author:
Dong Seok KIM
1
Author Information
1. Department of Neurosurgery, Yonsei University College of Medicine, Korea. dskim33@yuhs.ac
- Publication Type:Original Article
- Keywords:
Spinal dysraphism;
Neural tube defect;
Spina bifida
- MeSH:
Child;
Congenital Abnormalities;
Humans;
Joints;
Neural Tube Defects;
Specialization;
Spinal Cord;
Spinal Dysraphism;
Urinary Bladder
- From:Journal of the Korean Medical Association
2009;52(1):78-90
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
Spinal dysraphism is a common birth defect that causes different kinds of secondary impairments, including joint deformities, reduced mobility, and bowel or bladder dysfunction. Various dysraphic spinal abnormalities result in tethered cord syndrome, a progressive form of neurological deterioration that results from spinal cord tethering. The surgery and management of children who have spinal dysraphism require multidisciplinary care and long-term follow-up by multiple specialists in birth defects. This article reviews the clinical presentation, pathophysiology, diagnostic strategies, and therapeutic management of spinal dysraphism in infancy.