Amyopathic Dermatomyositis with Interstitial Lung Disease: A Case Report.
- Author:
Doo Hee LEE
;
Young Jun CHO
;
Jung Sik SONG
;
Chang Hee SEO
;
Jisoo LEE
;
Soo Kon LEE
- Publication Type:Case Report
- Keywords:
Amyopathic dermatomyositis;
Interstitial lung disease;
Immunoglobulim
- MeSH:
Dermatomyositis*;
Humans;
Immunoglobulins;
Lung Diseases, Interstitial*;
Prognosis
- From:The Journal of the Korean Rheumatism Association
1999;6(1):85-90
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
Amyopathic dermatomyositis is defined by characteristic cutaneous manifestation of dermatomyositis without evidence of muscle involvement. There is no clinical difference between dermatomyositis and amyopathic dermatomyositis. Pulmonary involvement of dermatomyositis is so frequent than aggressive dianostic and therapeutic approach is needed. Early steroid or immunosuppresive treatment in pulmonary involvement of dermatomyositis gets better prognosis. Intravenous immunoglobulin treatment is an effective and safe alternative when the steroid or immunosuppresive treatment is ineffective or intolerable. We are reporting a case of amyopathic dermatomyositis with interstitial lung disease. This patient was improved with intravenous immunoglobulin treatment.