Four cases of congenital absence of tracheal cartilage ring

VernacularTitle:先天性气管软骨环缺失4例
Author: Shuaishuai LIU ; Jing MA ; Shaochao WANG ; Zhiyu FENG ; Chao WANG ; Jinlu REN ; Chen MENG
From: Chinese Journal of Applied Clinical Pediatrics 2021;36(7):546-548
CountryChina
Language:Chinese
Abstract: The clinical data of 4 children with congenital absence of tracheal cartilage ring in Qilu Children′s Hospital of Shandong University from November 2017 to August 2019 were retrospectively analyzed.The age of the 4 cases was from 2 months to 1 year.One case had no obvious symptoms after birth, and then had repeated wheezing attacks for 3 times.Another 3 cases had symptoms after birth, such as throat ringing, repeated cough and asthma.Bronchoscopy in 4 cases indicated that the local lumen of trachea was round and centripetal stenosis, but the body of bronchoscope could pass smoothly, and no cartilage structure was found in the wall of trachea.Among them, 3 cases of chest enhanced CT examination displayed local and hourglass-like tracheal stenosis, without vascular ring malformation.All the 4 cases were treated by operation, of which 3 cases recovered well and 1 case died of severe infection after operation.